Presentation
Background of Arnold Chiari malformation type II
Patient Data
Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.
VP shunt in situ, colpocephaly, absent corpus callosum posteriorly - axial head CT
Sagittal: lifting up of the tentorium cerebellae and inferior tonsillar herniation. Small posterior fossa. No brain stem herniation. Note that the calvarium is not lemon shaped.
Case Discussion
A Chiari II malformation is a relatively common congenital malformation of the spine and posterior fossa characterized by lumbosacral spina bifeda aperta / myelomeningocoele and a small posterior fossa with descent of the brain stem. Numerous associated abnormalities are also frequently encountered.