Arrhythmogenic right ventricular cardiomyopathy
Updates to Case Attributes
There are multiple aneurysms of anterior wall in middle part of RV, which refers to structural abnormality of myocardium. RV ejection fraction 14%. There is also susceptibility artifact in tricuspid valve. RV apex contracts normal and does not have abnormal contrast enhancement.
T1can show cardial wall fat replacement in late stages of disease, but in this case there is only epicardial fat proliferation without reliable feature of intramyocardial fat.
The diagnosis of ARVC is based on the presence of major and minor criteria according to the revised Padua criteria (upgraded 2010 International Task Force).
In this case there are two major criteria:
1) dys/akynesis with aneurysmsaneurysmal RV walls
+ RV EDV/BSA 189mL/m2 (>100 mL/m2)
2))QRS=120ms
Also transmural contrast enhancement ofnoted in ≥1 RV region in delayed images.
-<p>There are multiple aneurysms of anterior wall in middle part of RV, which refers to structural abnormality of myocardium. RV ejection fraction 14%. There is also susceptibility artifact in tricuspid valve. RV apex contracts normal and does not have abnormal contrast enhancement.</p><p>T1 can show cardial wall fat replacement in late stages of disease, but in this case there is only epicardial fat proliferation without reliable feature of intramyocardial fat.</p><p>The diagnosis of ARVC is based on the presence of major and minor criteria according to the revised Padua criteria (upgraded 2010 International Task Force).</p><p>In this case there are two major criteria:</p><p>1) dys/akynesis with aneurysms RV walls </p><p> + RV EDV/BSA 189mL/m2 (>100 mL/m2)</p><p>2) transmural contrast enhancement of ≥1 RV region in delayed images.</p><p> </p>- +<p>There are multiple aneurysms of anterior wall in middle part of RV, which refers to structural abnormality of myocardium. RV ejection fraction 14%. There is also susceptibility artifact in tricuspid valve. RV apex contracts normal and does not have abnormal contrast enhancement.</p><p>T1 can show cardial wall fat replacement in late stages of disease, but in this case there is only epicardial fat proliferation without reliable feature of intramyocardial fat.</p><p>The diagnosis of ARVC is based on the presence of major and minor criteria according to the revised Padua criteria (upgraded 2010 International Task Force).</p><p>In this case there are two major criteria:</p><p>1) dys/akynesis with aneurysmal RV walls + RV EDV/BSA 189mL/m2 (>100 mL/m2)</p><p>2)QRS=120ms</p><p>Also transmural contrast enhancement noted in ≥1 RV region in delayed images.</p><p> </p>
Tags changed:
- arrhythmogenic right ventricular cardiomyopathy
- arvc
- arrhytmogenic cardiomyopathy
Updates to Freetext Attributes
The case is presented together with my colleagues: Anikin A., Barskiy V. and Basargina E.
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