Arrhythmogenic right ventricular cardiomyopathy
Updates to Case Attributes
There are multiple aneurysms of anterior wall in middle part of RV, which refers to structural abnormality of myocardium. RV ejection fraction 14%. There is also susceptibility artifact in tricuspid valve. RV apex contracts normal and does not have abnormal contrast enhancement.
T1 can show cardial wall fat replacement in late stages of disease, but in this case there is only epicardial fat proliferation without reliable feature of intramyocardial fat.
The diagnosis of ARVC is based on the presence of major and minor criteria according to the revised Padua criteria (upgraded 2010 International Task Force).
In this case, there are two major criteria (according to the Padua criteria):
1) dys/akynesis with aneurysmal RV walls
-
severe right ventricular dilation (dyskinetic and akinetic segments of the right ventricular free wall
+ RV EDV/BSA 189mL/m2 (>100 mL/m2)2)QRS=120msAlso - transmural
contrastlate gadolinium enhancementnotedin ≥1RVright ventricular regionin delayed images.
The case is presented together with my colleagues: Anikin A., Barskiy V. and Basargina E.
-<p>There are multiple aneurysms of anterior wall in middle part of RV, which refers to structural abnormality of myocardium. RV ejection fraction 14%. There is also susceptibility artifact in tricuspid valve. RV apex contracts normal and does not have abnormal contrast enhancement.</p><p>T1 can show cardial wall fat replacement in late stages of disease, but in this case there is only epicardial fat proliferation without reliable feature of intramyocardial fat.</p><p>The diagnosis of ARVC is based on the presence of major and minor criteria according to the revised Padua criteria (upgraded 2010 International Task Force).</p><p>In this case there are two major criteria:</p><p>1) dys/akynesis with aneurysmal RV walls + RV EDV/BSA 189mL/m2 (>100 mL/m2)</p><p>2)QRS=120ms</p><p>Also transmural contrast enhancement noted in ≥1 RV region in delayed images.</p><p> </p>- +<p>The diagnosis of ARVC is based on the presence of major and minor criteria according to the revised Padua criteria (upgraded 2010 International Task Force).</p><p>In this case, there are two major criteria (according to the Padua criteria):</p><ol>
- +<li>severe right ventricular dilation (dyskinetic and akinetic segments of the right ventricular free wall </li>
- +<li>transmural late gadolinium enhancement in ≥1 right ventricular region</li>
- +</ol><p> </p><p>The case is presented together with my colleagues: Anikin A., Barskiy V. and Basargina E.</p>
Updates to Study Attributes
- RV-EDVI: 189 mL/m2
- RV-EF: 13.9%
RightThe right ventricle (RV) is severely dilated, there is. There are dyskinesia and akynesiaakinesia of the middle and basal partparts of RVthe right ventricle with contrast enhancement onassociated late gadolinium enhancement serieswhich refer to a structural abnormality of the myocardium.
RV EDV/BSA 189mL/m2There is also a susceptibility artifact of the tricuspid valve after valve repair in early childhood.
RV EF 13.9%
Image MRI (Cine SSFP) ( update )
Image MRI (Cine SSFP) ( update )
Image MRI (Cine SSFP) ( update )
Image MRI (Cine SSFP) ( update )
Image MRI ( T1BB) ( update )
Image MRI (IRGRE) ( update )
Image MRI (IRGRE 15min) ( update )
Image 5 MRI ( T1BB) ( update )
Updates to Freetext Attributes
The case is presented together with my colleagues: Anikin A., Barskiy V. and Basargina E.
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