Presentation
Arrhythmia, exercise intolerance, dyspnea. Tricuspid annuloplasty at age of 9 months. Family history of sudden cardiac death.
Patient Data
- RV-EDVI: 189 mL/m2
- RV-EF: 13.9%
The right ventricle (RV) is severely dilated. There are dyskinesia and akinesia of the middle and basal parts of the right ventricle with associated late gadolinium enhancement which refer to a structural abnormality of the myocardium.
There is also a susceptibility artifact of the tricuspid valve after valve repair in early childhood.
Case Discussion
This is a case of ARVC based on the presence of two major criteria according to the revised Padua criteria 1:
In this case, there are two major criteria (according to the Padua criteria 1):
- severe right ventricular dilation (RV-EDVI > 100 mL/m2) with akinetic and dyskinetic bulging segments of the right ventricular free wall
- transmural late gadolinium enhancement in ≥1 right ventricular region
The case is presented together with my colleagues: Anikin A., Barskiy V. and Basargina E.