Arrhythmogenic right ventricular cardiomyopathy
Arrhythmia, exercise intolerance, dyspnea. Tricuspid annuloplasty at age of 9 months. Family history of sudden cardiac death.
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- RV-EDVI: 189 mL/m2
- RV-EF: 13.9%
The right ventricle (RV) is severely dilated. There are dyskinesia and akinesia of the middle and basal parts of the right ventricle with associated late gadolinium enhancement which refer to a structural abnormality of the myocardium.
There is also a susceptibility artifact of the tricuspid valve after valve repair in early childhood.
This is a case of ARVC based on the presence of two major criteria according to the revised Padua criteria 1:
In this case, there are two major criteria (according to the Padua criteria 1):
- severe right ventricular dilation (RV-EDVI > 100 mL/m2) with akinetic and dyskinetic bulging segments of the right ventricular free wall
- transmural late gadolinium enhancement in ≥1 right ventricular region
The case is presented together with my colleagues: Anikin A., Barskiy V. and Basargina E.
- 1. Corrado D, Perazzolo Marra M, Zorzi A, Beffagna G, Cipriani A, Lazzari M, Migliore F, Pilichou K, Rampazzo A, Rigato I, Rizzo S, Thiene G, Anastasakis A, Asimaki A, Bucciarelli-Ducci C, Haugaa KH, Marchlinski FE, Mazzanti A, McKenna WJ, Pantazis A, Pelliccia A, Schmied C, Sharma S, Wichter T, Bauce B, Basso C. Diagnosis of arrhythmogenic cardiomyopathy: The Padua criteria. (2020) International journal of cardiology. 319: 106-114. doi:10.1016/j.ijcard.2020.06.005 - Pubmed