Presentation
Occipital scalp swelling since birth.
Patient Data
Occipital midline subcutaneous cystic lesion connected by a stalk to the retrocerebellar dura via a small calvarial bone defect.
Occipital midline subcutaneous cystic lesion connected by a stalk to the retrocerebellar dura via a small calvarial bone defect.
Normal MRV study of the brain. No communication of the lesion with the cerebral venous system.
Case Discussion
Atretic cephaloceles are small, skin-covered scalp lesions that usually contain atretic brain tissue and meninges, which are usually situated in the parietal or occipital regions. They are considered rudimentary meningoceles or meningocele manqué. Histologically, they consist of residual dura or neuroglial rests, fibrovascular stalk, and embryonic vessels. Usually, there's a stalk connecting it to the dura intracranially via a calvarial bone defect.
On imaging, atretic cephalocele appears as a subcutaneous scalp cyst with a distinct connection to the dura and is associated with a calvarial bone defect.
- No communication with the cerebral venous system
- Persistent vertical embryonic positioning of the straight sinus is seen in a majority of cases (Persistent falcine vein)
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