Presentation
The patient came for assessment of hepatic cysts that was detected on ultrasonography. Family history of APCKD with end-stage renal disease.
Patient Data
Multiple variable-sized cysts are involving both kidneys and liver scattered throughout their parenchyma. The cysts show thin walls and homogeneous fluid density contents. The pancreas also shows small cysts. All cysts are seen of thin wall with fluid attenuation content.
Gallbladder stone seen impacted at the neck part.
Case Discussion
This case represents features of autosomal dominant polycystic kidney disease (ADPKD) with renal, liver, and pancreatic cysts. It usually ends with end-stage renal disease. Yet, in this case, there are still normal laboratory renal functions. Polycystic liver disease (PCLD) may occur in isolation or in patients with autosomal dominant polycystic kidney disease (ADPKD).