Autosomal dominant polycystic kidney disease associated with Caroli disease and pancreatic disease
Presented with abdominal pain and fever and jaundice.
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MRI of the abdomen (cronal reformats) demonstrates both kidneys markedly enlarged by multiple renal cysts ranging in size with saccular dilation of the intrahepatic billiary tree. There are also small cysts at pancreatic body.
MRCP demonstrates continuity with the biliary tree.
Caroli disease is associated with ADPKD and pancreatic cysts. Pancreatic cysts are more common in Von Hippel Lindau disease (VHL).