Band heterotopia

Case contributed by Dr Ayaz Hidayatov

Presentation

Seizures and mental retardation

Patient Data

Age: 5-10 years
Gender: Female
MRI

MR reveals a continuous band-like heterotopic grey matter seen just deep and paralleling the cortex separated from it with a thin layer of white matter. The signal intensity of heterotopic grey matter is the isointense to normal cortex on all sequences. The overlying cortex is mildly pachygyric.

There is also cerebellar vermian hypoplasia was noted. 

Case Discussion

The case demonstrates typical findings of band heterotopia or lissencephaly type 1-subcortical band heterotopia spectrum with double cortex sign.

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Case information

rID: 65065
Published: 22nd Dec 2018
Last edited: 15th Jun 2020
Inclusion in quiz mode: Included
Institution: Medistyle hospital