Bilateral Mondini malformations

Case contributed by Assoc Prof Frank Gaillard

CT through the temporal bones demonstrates a number of abnormalities of the labyrinth. The cochlea demonstrates only 1.5 turns. The basal turn is intact, however the more apical turns are absent replaced by a single cystic cavity. The vestibule is enlarged with normal semicircular canals and the vestibular aqueduct is enlarged.

Case Discussion

These features are characteristic of the Mondini malformation.

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Case information

rID: 5591
Published: 13th Feb 2009
Last edited: 13th Aug 2019
System: Head & Neck
Inclusion in quiz mode: Included

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