Cardiac amyloidosis

Case contributed by Dr Jayanth Keshavamurthy

Presentation

History of bi-atrial enlargement, biventricular hypertrophy, systolic and diastolic dysfunction on echocardiogram. Cardiac MRI was positive for an infiltrative cardiomyopathy.

Patient Data

Age: 70 years
Gender: Male
Nuclear medicine

Nuclear medicine scan strongly positive for transthyretin amyloid cardiomyopathy (ATTR-CM).

Semi-quantitative Perugini grading scale  is 3.0

The ROI ratio is 1.9 (> 1.5 is positive).

Case Discussion

The patient is waiting for myocardial biopsy for corrective treatment. Work up for myeloma and systemic amyloidosis is negative.

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Case information

rID: 80705
Published: 5th Aug 2020
Last edited: 9th Aug 2020
System: Cardiac
Inclusion in quiz mode: Included
Institution: Augusta University

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