Presentation
Patient with severe left ventricular hypertrophy, bi-atrial enlargement, systolic dysfunction and BNP >8000. Cardiac MRI was negative for cardiac amyloidosis.
Patient Data
Age: 70 years
Gender: Male
{"current_user":null,"step_through_annotations":true,"access":{"can_edit":false,"can_download":true,"can_toggle_annotations":true,"can_feature":false,"can_examine_pipeline_reports":false,"can_pin":false},"extraPropsURL":"/studies/94149/annotated_viewer_json?lang=us"}
Semi-quantitative Perugini grading scale is 3.0.
The ROI Ratio is 1.7 and positive for ATTR cardiac amyloidosis.
Case Discussion
The patient is currently waiting for a cardiac biopsy for confirmation and corrective treatment.
Work up for myeloma and systemic amyloidosis is negative.
One can get a positive nuclear medicine scan despite normal cardiac MRI. So one needs to know the sensitivity and specificity for each of these modalities and how to use them and order them appropriately.
New treatments are available now for ATTR-cardiac amyloidosis.
Unable to process the form. Check for errors and try again.