Cardiac amyloidosis

Case contributed by Dr Jayanth Keshavamurthy

Presentation

Patient with severe left ventricular hypertrophy, bi-atrial enlargement, systolic dysfunction and BNP >8000. Cardiac MRI was negative for cardiac amyloidosis.

Patient Data

Age: 70 years
Gender: Male
Nuclear medicine

The semi-quantitative score is 3.0.

The ROI Ratio is 1.7 and positive for ATTR cardiac amyloidosis.

Case Discussion

The patient is currently waiting for a cardiac biopsy for confirmation and corrective treatment.

Work up for myeloma and systemic amyloidosis is negative.

One can get a positive nuclear medicine scan despite normal cardiac MRI. So one needs to know the sensitivity and specificity for each of these modalities and how to use them and order them appropriately.

New treatments are available now for ATTR-cardiac amyloidosis.

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Case information

rID: 80704
Published: 20th Aug 2020
Last edited: 26th Aug 2020
System: Cardiac
Inclusion in quiz mode: Included
Institution: Augusta University

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