Caroli disease

Case contributed by Dr Michael P Hartung

Presentation

Liver transplant evaluation.

Patient Data

Gender: Female
mri

Extensive ectasia of the biliary tree throughout the liver, some dilated ducts with a characteristic central dot coursing through (fibrovascular bundle). Splenomegaly and extensive varices. Abnormal kidneys with dysplastic cortex indicating medullary sponge kidney (known association). 

ct

Preceding flank pain CT showing findings of biliary ectasia and abnormal renal morphology. 

Case Discussion

Typical findings of Caroli disease on MRI and CT, with renal association of medullary sponge kidney. These images were obtained as part of a pre-liver transplant workup. 

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