Caroli disease with medullary sponge kidney and nephrocalcinosis

Case contributed by Dr Paresh K Desai

Presentation

Obstructive jaundice

Patient Data

Age: 35 years
Gender: Male

Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.

MRI reveals intrahepatic and extrahepatic cystic dilatations of biliary tract with multiple large calculi.

Incidental detection of medullary sponge kidney.

Case Discussion

MRI reveals intrahepatic and extrahepatic cystic dilatations of the biliary tract with multiple large calculi. Incidental detection of medullary sponge kidney. Renal USG performed subsequently also revealed nephrocalcinosis.

Isolated case reports of association of Caroli disease with renal cystic disease are scattered in the English literature. There is also an association of oro-facial-digital syndrome with cystic disease of the kidneys and the biliary tree.

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