Chiari I malformation with dorso-lumbar syrinx

Case contributed by Dr Maxime St-Amant

Presentation

Patient known with Chiari I malformation. R/o syrinx.

Patient Data

Age: 2 years
Gender: Male

Sagittal T1 & T2 MRI of the spine shows a dorso-lumbar syrinx with herniated cerebellar tonsils, in a patient with known Chiari I malformation. Although more than 20 % of patients with a Chiari I malformation have an associated syrinx, they usually are located in the cervical spine. This case demonstrates a dorsolumbar syrinx associated with Chiari I.

A ventriculus terminalis would present like this, except less voluminous, and located distally (as the name says it, at the filum terminalis).

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Case information

rID: 18924
Case created: 27th Jul 2012
Last edited: 30th Jan 2016
Inclusion in quiz mode: Excluded

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