Chiari I malformation with syrinx

Case contributed by Dr Mostafa El-Feky


Muscle weakness.

Patient Data

Age: 5 years
Gender: Female

MRI cervical spine

There is cerebellar tonsils descent through foramen magnum compressing the cervicomedullary junction with resultant whole spinal cord syrinx. No associated hydrocephalic changes.


Annotated images

The tonsillar herniation is estimated to be 7.2 mm below the foramen magnum (Chiari 1 malformation >6 mm).

Case Discussion

Child with a Chiari 1 malformation and resulting extensive syrinx involving the whole spinal cord (Holocord presentation).

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Case information

rID: 56514
Published: 13th Nov 2017
Last edited: 21st Nov 2019
Inclusion in quiz mode: Included
Institution: Dar El Ashaa Center

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