Chiari II malformation

Case contributed by Dr Amr Farouk

Presentation

1-month-old neonate presenting with myelomeningocele for CNS survey.

Patient Data

Age: 1 month old
Gender: Female
MRI

Infra-tentorial findings:

  • Crowded foramen magnum with the cerebellar tonsils and vermis seen displaced inferiorly.
  • Small posterior fossa with a low attachment of the tentorium and low torcula.
  • Pulled down brainstem with an elongated and low lying fourth ventricle.
  • Tectal plate beaking.
  • Angulation of the aqueduct.
  • Concavity of clivus

Supratentorial findings:

Case Discussion

The constellation of the supra and infra-tentorial CNS findings in addition to the myelomeningocele are of a Chiari II malformation.

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Case information

rID: 58484
Published: 19th Feb 2018
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included
Institution: National cancer institute, Cairo, Egypt

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