Chiari II malformation

Case contributed by A.Prof Frank Gaillard

Presentation

Long history of neurological impairment since birth.

Patient Data

Age: 20 years
Gender: Female

MRI brain

Modality: MRI

MRI of the brain demonstrates a small posterior fossa with low lying tentorial attachment posteriorly. The tectum is beaked and hydrocephalus is present. 

MRI cervical spine

Modality: MRI

The low lying tonsils in the foramen magnum are noted and the the cervical spine shows a local syrinx between C6 - T2. Additionally the C3 and C4 vertebral bodies are congenitally fused. 

MRI lumbar spine

Modality: MRI

The lumbar spine shows the tethered cord down to the meningomyelocele at the level of S1 - S3. No abnormality is seen to the overlying subcutaneous fat. 

Case Discussion

This case illustrates many of the common features of Chiari II malformations, particularly the presence of a lumbosacral myelomeningocoele, small posterior fossa with tectal beaking and hydrocephalus. In this case the corpus callosum is intact. 

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Case Information

rID: 16050
Case created: 11th Dec 2011
Last edited: 14th Feb 2017
Inclusion in quiz mode: Included

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