Chiari II malformation with spinal meningomyelocele

Case contributed by Dr Mohammad A. ElBeialy


Newborn female with lower back cystic lesion.

Patient Data

Age: 15 days
Gender: Female
  • spinal dysraphism with defective posterior elements of the dorsal and lumbo-sacral spine.
  • a large multi-septated sac is seen continuous with the bony spinal canal, it measures about 6 X 3 X 1.5 cm and deformity low T2 and high T2 signal. 
  • a relatively large cord syrinx is seen within the dorsal cord and blinding within the dorso-lumbar sac (myelomeningocele). 
  • neurogenic bladder with marked dilatation and bilateral hydroureteronephrosis. 
  • marked bilateral supratentorial hydrocephalic changes. 
  • dysplastic posterior fossa with crowding of its contents.

Case Discussion

Chiari II malformation with large spinal dysraphism, spinal myelomeningocele and cord syrinx, marked supratentorial hydrocephalus as well as neurogenic bladder with bilateral hydroureteronephrosis.

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Case information

rID: 23550
Published: 23rd Jun 2013
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included