Presentation
Jaundice and vague upper abdominal pains.
Patient Data
Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.
Case Discussion
Choledochal cysts are congenital conditions associated with benign cystic dilatation of bile ducts. They are uncommon in Western countries but not as rare in East Asian nations like Japan and China.
They were classified into 5 types by Todani in 1977.
The classification was based on the site of the cyst or dilatation.
type I: most common variety involving saccular or fusiform dilatation of a portion or entire common bile duct (CBD) with normal intrahepatic bile ducts
type II: isolated diverticulum protruding from the CBD
type III or choledochocele: arises from dilatation of the duodenal portion of CBD or where the pancreatic duct meets
type IV: dilatation of both intrahepatic and extrahepatic biliary ducts
type V or Caroli disease: cystic dilatation of intrahepatic biliary ducts