Chronic Budd-Chiari syndrome

Case contributed by Fazel Rahman Faizi
Diagnosis almost certain

Presentation

Abdominal distension.

Patient Data

Age: 30 years
Gender: Female

The hepatic veins cannot be identified. 
The intra-hepatic portion of the inferior vena cava reveals narrow caliber.
The liver shows irregular contour with an inhomogeneous and mottled appearance.
The caudate is significantly enlarged.
The portal vein is dilated, measured 21 mm in diameter. No evidence of thrombosis.
The spleen is homogeneously enlarged in size without focal lesion.
Mild free fluid is noted in the perihepatic region as well as in the pelvis. ​

Case Discussion

The features are compatible with chronic Budd Chiari syndrome complicated by portal venous hypertension. Hypertrophy of the caudate lobe is an indicator of chronicity of the disease.

Dr. Mohammed Tahir Aien has also contributed to this case.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.