Cirrhosis in a patient with autosomal dominant polycystic kidney disease
Presentation
Work up for abdominal pain and elevated liver enzymes.
Patient Data
The liver has an irregular margin inferring cirrhosis. A few small cysts, less than 17 mm, are seen in the liver. No enhancing hepatic mass is identified in the current study.
Multiple dilated collateral vessels are present at peripancreatic and perigastric regions as well as around the splenic hilum, consistent with portal hypertension.
The spleen is markedly enlarged, and its cephalocaudal height measured 293 mm.
Multiple small hyper-dense stones are seen in the gallbladder.
Multiple simple cortical cysts are seen in the kidneys less than 40 mm, most consistent with autosomal dominant polycystic kidney disease.
Small fat containing para-umbilical hernia is noted.
Case Discussion
Cirrhosis with evidence of portal hypertension and huge splenomegaly in a patient with autosomal dominant polycystic kidney disease (ADPKD).
Several conditions are well recognized as associated with ADPKD, such as hepatic cysts, but cirrhosis has not been reported as an association.
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