Congenital aqueduct stenosis producing the "sunset eye" sign

Case contributed by Dr Chris O'Donnell

Presentation

Past history of spina bifida. Large head with frontal bossing and downturned eyes

Patient Data

Age: 19 months
Gender: Male

Marked dilatation of lateral and 3rd ventricles and normal size 4th ventricle secondary to aqueductal stenosis.

Case Discussion

Typical aqueduct stenosis characterized by a septum or diaphragm obstructing the lumen with gross lateral and 3rd ventricular dilatation.  Enlarged head with frontal bossing (i.e. enlarged supratentorium and small posterior fossa) and downturning of the globes characterized by the lenses pointing down rather than forward.

PlayAdd to Share

Case information

rID: 19842
Case created: 16th Oct 2012
Last edited: 7th Feb 2016
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.