Congenital aqueduct stenosis producing the "sunset eye" sign

Case contributed by Chris O'Donnell
Diagnosis almost certain

Presentation

Past history of spina bifida. Large head with frontal bossing and downturned eyes

Patient Data

Age: 19 months
Gender: Male

Marked dilatation of lateral and 3rd ventricles and normal size 4th ventricle secondary to aqueductal stenosis.

Case Discussion

Typical aqueduct stenosis characterized by a septum or diaphragm obstructing the lumen with gross lateral and 3rd ventricular dilatation.  Enlarged head with frontal bossing (i.e. enlarged supratentorium and small posterior fossa) and downturning of the globes characterized by the lenses pointing down rather than forward.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.