Congenital aqueduct stenosis producing the "sunset eye" sign

Case contributed by Dr Chris O'Donnell


Past history of spina bifida. Large head with frontal bossing and downturned eyes

Patient Data

Age: 19 months
Gender: Male

Marked dilatation of lateral and 3rd ventricles and normal size 4th ventricle secondary to aqueductal stenosis.

Case Discussion

Typical aqueduct stenosis characterized by a septum or diaphragm obstructing the lumen with gross lateral and 3rd ventricular dilatation.  Enlarged head with frontal bossing (i.e. enlarged supratentorium and small posterior fossa) and downturning of the globes characterized by the lenses pointing down rather than forward.

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Case information

rID: 19842
Published: 16th Oct 2012
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

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