Presentation
Past history of spina bifida. Large head with frontal bossing and downturned eyes
Patient Data
Age: 19 months
Gender: Male
From the case:
Congenital aqueduct stenosis producing the "sunset eye" sign
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Marked dilatation of lateral and 3rd ventricles and normal size 4th ventricle secondary to aqueductal stenosis.
Case Discussion
Typical aqueduct stenosis characterized by a septum or diaphragm obstructing the lumen with gross lateral and 3rd ventricular dilatation. Enlarged head with frontal bossing (i.e. enlarged supratentorium and small posterior fossa) and downturning of the globes characterized by the lenses pointing down rather than forward.