Congenital diaphragmatic hernia

Case contributed by Tim Luijkx
Diagnosis certain

Presentation

Respiratory distress immediately after birth, pulmonary hypertension. Intubated.

Patient Data

Age: 1 day
Gender: Female
x-ray

Large diaphragmatic hernia with intrathoracic herniation of intestines and part of liver, as demonstrated by intrathoracic position of venous umbilical catheter. Mediastinal shift.

Case Discussion

Large congenital diaphragmatic hernia with intrathoracic position of intestines and liver. Right lung turned out to be hypoplastic

Operative closure of the diaphragmatic defect. Initially only skin was closed because of a mismatch between abdominal cavity volume and contents, increasing the risk of abdominal compartment syndrome, hence leaving an abdominal wall hernia.

Pulmonary hypertension disappeared. Abdominal wall to be closed later.

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