Congenital extrahepatic portosystemic shunt

Case contributed by Ameen Rageh , 7 Jan 2018
Diagnosis probable
Changed by Ameen Rageh, 7 Jan 2018
Hidden edits. Some edits not affecting the appearance of this case have been suppressed.

Updates to Case Attributes

Title was changed:
Congenital Extrahepatic Portosystemic Shuntextrahepatic portosystemic shunt
Status changed from draft to pending review.

References changed:

  • Gallego C, Velasco M, Marcuello P, Tejedor D, De Campo L, Friera A. Congenital and acquired anomalies of the portal venous system. (2002) Radiographics : a review publication of the Radiological Society of North America, Inc. 22 (1): 141-59. <a href="https://doi.org/10.1148/radiographics.22.1.g02ja08141">doi:10.1148/radiographics.22.1.g02ja08141</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/11796904">Pubmed</a> <span class="ref_v4"></span>
  • Wai-Kit Lee, Silvia D. Chang, Vinay A. Duddalwar, Jules M. Comin, Warren Perera, Wing-Fai E. Lau, Elhamy K. Bekhit, Oliver F. Hennessy. Imaging Assessment of Congenital and Acquired Abnormalities of the Portal Venous System. (2011) RadioGraphics. 31 (4): 905-26. <a href="https://doi.org/10.1148/rg.314105104">doi:10.1148/rg.314105104</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/21768231">Pubmed</a> <span class="ref_v4"></span>
  • Alonso-Gamarra E, Parrón M, Pérez A, Prieto C, Hierro L, López-Santamaría M. Clinical and radiologic manifestations of congenital extrahepatic portosystemic shunts: a comprehensive review. (2011) Radiographics : a review publication of the Radiological Society of North America, Inc. 31 (3): 707-22. <a href="https://doi.org/10.1148/rg.313105070">doi:10.1148/rg.313105070</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/21571652">Pubmed</a> <span class="ref_v4"></span>
  • Gallego C, Velasco M, Marcuello P, Tejedor D, De Campo L, Friera A. Congenital and acquired anomalies of the portal venous system. Radiographics. 2002 Jan;22(1):141-59.
  • Lee WK, Chang SD, Duddalwar VA, Comin JM, Perera W, Lau WF, Bekhit EK, Hennessy OF. Imaging assessment of congenital and acquired abnormalities of the portal venous system. Radiographics. 2011 Jul 8;31(4):905-26.
  • Alonso-Gamarra E, Parrón M, Pérez A, Prieto C, Hierro L, López-Santamaría M. Clinical and radiologic manifestations of congenital extrahepatic portosystemic shunts: a comprehensive review. Radiographics. 2011 May 4;31(3):707-22.

Updates to Study Attributes

Findings was changed:

CT scan abdomen with contrast acquired during portal phase show, a hypoplastic portal vein. A large tortuous vein is seen communicating between the splenic vein and left renal vein consistent with Splenorenal shunt. 

Abdominal subcutaneous edema with dilated second left lumbar and subcutaneous veins. 

NO FINDING SUGGESTING CHRONIC LIVER CIRRHOSISNo finding suggesting chronic liver cirrhosis 

SPLEEN SIZE IS NORMALSpleen size is normal 

NO ASCITES No ascites

Conclusion:

IN THE ABSENCE OF SIGNS OF CHRONIC LIVER DISEASE/PORTAL HYPERTENSION FINDING ARE SUGGESTING OF CONGENITAL EXTRAHEPATIC PORTOSYSTEMIC SHUNT (TYPEIn the absence of signs of chronic liver disease/portal hypertension findings are suggesting of congenital extrahepatic portosystemic shunt (type 2).

Images Changes:

Image CT (MIP along axis of portal vein) ( update )

Specifics was set to MIP along axis of portal vein.

Image 5 CT (MIP along axis of portal vein) ( create )

Position was set to .

Image 6 CT (MIP) ( update )

Position was set to .

Image 7 CT (3D) ( update )

Position was set to .

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.