Congenital lobar emphysema

Case contributed by Dr Domenico Nicoletti

Presentation

Dyspnoea, tachycardia, cyanosis.

Patient Data

Age: 4 months
Gender: Male
Modality: X-ray

Hyperinflation and poor vascularization of left upper lobe with contralateral mediastinal shift.

Modality: CT

Hyperinflation and poor vascularization of left upper lobe with contralateral mediastinal shift.

Modality: X-ray

Post upper lobectomy.

Case Discussion

Congenital lobar emphysema (CLE) is the overinflation of one or more lung lobes, present from birth with a lung histologically normal. The left upper lobe is most frequently affected. 

The causes are varied but are all linked to an abnormal intrauterine development. The common mechanism includes obstruction of a lobar or segmental bronchus with valve mechanism that results in gas trapping with overdistension of the lung and tissue destruction.

Acknowledgment: Dr Maurizio Salvi.

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Case Information

rID: 37234
Case created: 29th May 2015
Last edited: 18th Dec 2015
Systems: Chest, Paediatrics
Inclusion in quiz mode: Included

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