Congenital lobar emphysema

Case contributed by Domenico Nicoletti
Diagnosis certain

Presentation

Dyspnea, tachycardia, cyanosis.

Patient Data

Age: 4 months
Gender: Male
x-ray

Hyperinflation and poor vascularization of left upper lobe with contralateral mediastinal shift.

ct

Hyperinflation and poor vascularization of left upper lobe with contralateral mediastinal shift.

x-ray

Post upper lobectomy.

Case Discussion

Congenital lobar emphysema (CLE) is the overinflation of one or more lung lobes, present from birth with a lung histologically normal. The left upper lobe is most frequently affected. 

The causes are varied but are all linked to abnormal intrauterine development. The common mechanism includes obstruction of a lobar or segmental bronchus with valve mechanism that results in gas trapping with overdistension of the lung and tissue destruction.

Acknowledgement: Dr Maurizio Salvi.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.