IMPORTANT: We currently have a number of bugs related to image cropping and are actively trying to resolve them. In the meantime, we have disabled cropping. Apologies for any inconvenience. Stay informed: radiopaedia.org/chat

Congenital pulmonary airway malformation

Case contributed by Yaïr Glick
Diagnosis certain

Presentation

Suspicion of CPAM on prenatal ultrasound.

Patient Data

Age: Neonate
Gender: Female

CXR at age 0 days

x-ray

Chest X-ray taken on the day of birth.

Central opacities. Right perihilar lucencies, more prominent (pseudocystic) in the upper zone. The differential diagnosis includes CPAM.
No pleural effusion.
Cardiac silhouette normal, small thymus.

CXR at age 6 months

x-ray

Chest X-ray taken at age 6 months.

Large cystic lesion in the RLL.
Left lung well aerated.
Cardiac silhouette of normal size.

The upper segment of the RLL is very large and is composed of cysts of different sizes, ranging up to a diameter of 2.5 cm. The entire lesion measures 4.8 x 4.1 x 4.7 cm. Mild adjacent pleural thickening. No soft tissue component or abnormal vasculature. Small RUL atelectasis. Small atelectases in the dependent portions. Mild tracheal compression anteriorly by the brachiocephalic artery.

In summary: features consistent with CPAM.

Case Discussion

Pathology report:

Upper segment right lower lobe:
Features compatible with congenital cystic adenomatoid malformation, type I.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.