Congenital pulmonary airway malformation

Case contributed by Dr Aliakbar Sahraei


A term neonate who developed respiratory distress after delivery.

Patient Data

Age: 2 days
Gender: Female

Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.

Chest radiograph demonstrates a large left sided multicystic (air-filled) lesion with marked mediastinal shift to the right and depression of the left hemidiaphragm. Differentials for this appearance would include CPAM and congenital lobar emphysema. Congenital diaphragmatic hernia is less likely given the air-filled stomach and intestinal loops in the abdomen.

Selected CT images of the chest confirm a large multicystic lesion which almost entirely occupies the left lung with marked midline shift to the right. Many of the cysts measure more than 2 cm, in keeping with a large type I CPAM lesion.

Case Discussion

A case of type I congenital pulmonary airway malformation

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