Congenital pulmonary airway malformation and duplication cyst

Case contributed by Jane McEniery
Diagnosis almost certain


3 month old female who presents for follow up of a finding on antenatal imaging.

Patient Data

Age: 3 months
Gender: Female
  • Cluster of thin walled cystic spaces in the superior segment left lower lobe
  • A low attenuation region of lung extends inferiorly to the level of the diaphragm, 
  • Atelectasis adjacent the cystic lesion and within the dependent portions of the right lung
  • Aorta has a normal appearance with no visible aberrant vessel supplying this region 
  • NG with tip in the stomach, with contrast within the stomach lumen
  • Homogeneous hypodense round filling defect posterolateral to the gastro-esophageal junction
  • Normal appearance of the upper abdominal viscera and skeletal structures

Case Discussion

The cystic lesion is consistent with a congenital pulmonary airway malformation.  The hypodense lesion within the stomach is consistent with a duplication cyst.

The histological diagnosis of congenital airway pulmonary malformation (CPAM) was confirmed following left lower lobectomy. The duplication cyst has not been resected.

Case contributed by Dr Jonathan Corness.

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