Congenital pulmonary airway malformation (CPAM)

Case contributed by Mohammad Hadi Akbarizadeh
Diagnosis possible

Presentation

Cough and dyspnea.

Patient Data

Age: 60 years
Gender: Male

A multiloculated cystic mass measuring 31 x 28 mm in the anterior left upper lobe is compatible with congenital pulmonary airway malformation (CPAM).

There is also air trapping in the right lower lobe.

Case Discussion

Congenital pulmonary airway malformations (CPAM) also known as congenital cystic adenomatoid malformation (CCAM) are multicystic masses of segmental lung tissue with abnormal bronchial proliferation. Five subtypes are currently classified and type 1 is most common type. At antenatal ultrasound it appears as an isolated cystic or solid intrathoracic mass.

Surgery is the treatment of choice in symptomatic patients, both in those presenting early with respiratory compromise and in those presenting later with recurrent infections. Type I lesions have the best prognosis.

I would like to sincerely thank my professor Dr Adele Dadkhah for the helping with diagnosis and the report.

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