Congenital pulmonary airway malformation - type I

Case contributed by Dr Praveen Jha


Recurrent pneumonia, breathlessness. Previous chest radiograph showed possible diaphragmatic hernia.

Patient Data

Age: 1.5
Gender: Female

Large cystic areas in right hemithorax with some of them showing air-fluid levels, with contralateral mediastinal shift. Diaphragmatic outline is not well visualized on right side. Possibility of diaphragmatic hernia was being considered.

Multiple cystic areas of varying sizes, reaching upto 8 cm in size are seen replacing most of the lung parenchyma. Residual lung parenchyma appears compressed and atelectatic. Contralateral tracheomediastinal shift is seen. Diaphragmatic continuity appears intact.

A post-contrast radiograph taken, also shows above mentioned findings.

Case Discussion

Congenital pulmonary airway malformation type I, has large cystic areas, which may have air-fluid levels. Also, these large cysts may produce mass effect and mediastinal shift, which may be confused with congenital diaphragmatic hernia on a radiograph. Cross-sectional imaging helps in this regard.


(Case courtesy: Dr. Abhijit Yadav, Dr. B L Yadav center for diagnostic imaging and research)

PlayAdd to Share

Case information

rID: 29982
Published: 9th Jul 2014
Last edited: 11th Jul 2020
System: Chest
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.