Congenital pulmonary airways malformation

Case contributed by Dr Aliakbar Sahraei

Presentation

A term neonate who developed respiratory distress after delivery.

Patient Data

Age: 2 days
Gender: Female

Chest radiography demonstrates a large left sided multicystic (air-filled) lesion with marked mediastinal shift to the right and depression of the left hemidiaphragm. Differentials for this appearance would include CPAM or congenital lobar emphysema. Congenital diaphragmatic hernia thought less likely given the air filled stomach and intestinal loops in the abdomen. 

Selected CT images of the chest confirms a large multicytic lesion which almost entirely occupies the left lung with marked midline shift to the right. Many of the cysts measure more than 2 cm. This would be in keeping with a large type I CPAM lesion.

Case Discussion

A case of type I congenital pulmonary airway malformation

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Case information

rID: 34607
Published: 30th Jul 2015
Last edited: 5th Oct 2019
Inclusion in quiz mode: Excluded

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