Congenital pulmonary airways malformation

Case contributed by Dr Ahmed Abd Rabou

Presentation

Neonate with respiratory distress and abnormal chest x ray.

Patient Data

Age: 2 days old
Gender: Female

The upper lobe of the left lung is occupied by multiple large size cysts causing relaxation collapse of the lower lobe and rightward mild mediastinal shift. The diaphragm is intact.

Diagnosis: congenital cystic adenomatoid malformation CCAM type I

Case Discussion

CCAM or CPAM are spectrum of cystic diseases involving the pulmonary airways. Other differential consideration of neonatal cystic pulmonary lesion includes congenital diaphragmatic hernia, congenital lobe emphysema, pulmonary sequestration and bronchogenic cyst
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Case information

rID: 25491
Case created: 27th Oct 2013
Last edited: 1st Jul 2017
Systems: Chest, Paediatrics
Tags: lung, cysts
Inclusion in quiz mode: Included

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