Congenital pyriform aperture stenosis

Case contributed by Dr Charlie Chia-Tsong Hsu

Presentation

Breathing difficulties worse with feeding.

Patient Data

Age: 6 weeks old.
Gender: Female

Non contrast CT paranasal sinuses demonstrate abnormal thickening and medialisation of anterior maxillae resulting in narrowing of nasal airway. The width of the nasal airway at the narrowest point is measures less than 11 mm. Imaging findings is consistent with congenital pyriform aperture stenosis. Associated abnormal dentition with presence of solitary median maxillary central incisor (SMMCI) resulting in mal-alignment of the normal central and lateral maxillary incisors.

Neonatal MRI examination was normal (not shown). No midline brain abnormality. 

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Case information

rID: 30223
Case created: 27th Jul 2014
Last edited: 19th Dec 2015
System: Paediatrics
Inclusion in quiz mode: Included

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