Congenital venolobar syndrome

Case contributed by Dr Rachael O'Rourke


Known congenital heart disease patient with scimitar syndrome undergoing routine imaging work up for planning of surgical repair.

Patient Data

Gender: Female

Pulmonary MRA demonstrates large right sided scimitar vein draining to the IVC. A small systemic vessel arises from the aorta on the right and supplies the posterobasal segment of the right lower lobe, with a difference in perfusion seen within this pulmonary segment as a result. This represents a right lower lobe sequestration.

Incidental breast prostheses.

Case Discussion

Congenital venolobar syndrome in a young female patient, with large scimitar vein and right lower lobe pulmonary sequestration. Identification of the systemic vessel arising from the aorta is important for surgical planning, enabling the surgeon to avoid injury to the vessel and decrease perioperative risk.

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Case information

rID: 44466
Published: 7th Oct 2016
Last edited: 7th Oct 2016
System: Chest, Vascular
Inclusion in quiz mode: Excluded

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