Presentation
One week history of behavioral changes and expressive dysphasia. Otherwise normal neurological examination.
Patient Data
Agenesis of corpus callosum is noted with lack of rostrum, genu, body, isthmus and splenium. Colpocephaly is seen with dilatation of the occipital horns bilaterally and prominence of temporal horns. On the coronal series the lateral ventricles resemble the Viking helmet of Texas long horn. Absent cingulate sulcus. Upward extension of the third ventricle into the inter hemispheric fissure is also noted. Loculated hyperintense CSF fluid filled areas are noted in the posterior fossa bilaterally.