Craniofacial fibrous dysplasia

Case contributed by Dr Ian Bickle

Presentation

10 year old with increasing lump on scalp. Trauma 2 months previously.

Patient Data

Age: 10
Gender: Female
CT

Sclerotic expansile groundglass appearances to the left zygomatic process extending to the frontozygomatic suture.  This extends to involve the superior orbital margin and to a lesser extent the greater wing of sphenoid.

No cortical breech.

No soft tissue component.

Bilateral maxillary sinusitis.

Case Discussion

Lesson number one of radiology - take the clinical history with a pinch of salt.

This case has the typical appearances of fibrous dysplasia in a patient with the correct demographics for the disease.

  • smooth groundglass change to the bone
  • sharp delineation of the pathological and normal bone (narrow zone of transition)
  • expansile and sclerotic in nature
  • typical craniofacial location
  • cortex remains intact
PlayAdd to Share

Case information

rID: 47431
Published: 17th Aug 2016
Last edited: 16th Jul 2018
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.