Craniofacial fibrous dysplasia

Case contributed by Dr Ian Bickle

Presentation

10 year old with increasing lump on scalp. Trauma 2 months previously.

Patient Data

Age: 10
Gender: Female
CT

Sclerotic expansile groundglass appearances to the left zygomatic process extending to the frontozygomatic suture.  This extends to involve the superior orbital margin and to a lesser extent the greater wing of sphenoid.

No cortical breech.

No soft tissue component.

Bilateral maxillary sinusitis.

Case Discussion

Lesson number one of radiology - take the clinical history with a pinch of salt.

This case has the typical appearances of fibrous dysplasia in a patient with the correct demographics for the disease.

1. Smooth groundglass change to the bone

2. Sharp delineation of the pathological and normal bone (narrow zone of transition)

3. Expansile and sclerotic in nature

4. Typical craniofacial location

5.  Cortex remains intact

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Case information

rID: 47431
Case created: 16th Aug 2016
Last edited: 27th Sep 2016
Inclusion in quiz mode: Included

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