Presentation
Cranial deformity.
Patient Data
Premature closure of the left coronal suture with flattening of the ipsilateral frontal region as well as elevated superolateral corner of the left orbit "harlequin eye deformity".
Normal appearance of the other cranial sutures.
Case Discussion
CT features characteristic of a unilateral premature closure of the coronal suture (frontal plagiocephaly).
Craniosynostosis refers to the premature fusion of one or more cranial sutures. They can occur as a primary abnormality (developmental error during embryogenesis) or secondary (mechanical causes such as intrauterine compression, and metabolic causes).
The average age of coronal suture closure is around 24 years.
Coronal synostosis (plagiocephaly) is the second most common type after sagittal synostosis (scaphocephaly). It should not be confused with positional plagiocephaly. which is considered a calvarial deformity that results from external pressure and not from premature suture synostosis.