Crossed fused renal ectopia
Citation, DOI, disclosures and case data
At the time the case was submitted for publication Mark D. Sugi had no recorded disclosures.View Mark D. Sugi's current disclosures
History of HIV and chronic hemolytic anemia with portal vein thrombosis. Presents with concern for abdominal infection.
Loading Stack -
0 images remaining
Contrast-enhanced CT images show inferior crossed fused renal ectopia with fusion of the ectopic left kidney to the inferior right kidney. Both ureters arise anteriorly with the ureter of the right kidney draining into the right ureterovesical junction, and the ureter of the ectopic left kidney draining into the left ureterovesical junction.
Vascular anatomy: The artery supplying the ectopic left kidney arises from the right common iliac artery and there is separate venous drainage of the ectopic left kidney into the inferior vena cava (IVC), medial and inferior to the junction of the right renal vein and IVC.
Multiple non-obstructive renal calculi and cyst in the ectopic left kidney. Prostatomegaly.
Additional findings: cirrhosis of unknown etiology with thrombosis and early cavernous transformation of the main portal vein. Sequela of portal hypertension, including small volume ascites and small esophageal/paraesophageal varices.
This represents the most common form of crossed fused renal ectopia (type A). This congenital anomaly is often asymptomatic and detected incidentally on imaging performed for other reasons or at antenatal sonography. Symptomatic patients generally present in the setting of vesicoureteral reflux, obstructive renal calculi, or urinary tract infection.
- 1. Crossed fused renal ectopia: Diagnosis and prognosis as a single-center experience. (2020) Journal of Pediatric Surgery. doi:10.1016/j.jpedsurg.2020.08.030