CSF leak from meningocoele in Marfan's disease

Case contributed by A.Prof Frank Gaillard

Presentation

Headaches worse on standing.

Patient Data

Age: 17 years
Gender: Female
Modality: MRI

Diffuse dural ectasia presumably related to the patient's known Marfan's syndrome expands the central vertebral canal. This expansion is most pronounced in the sacral spine, where it is continuous with large CSF intensity structures extending through the sacral foramina. The sacrum is thinned as a result. Some of the structures extend beyond the sacral foramina anteriorly, most pronounced at S1 on the right. 

The likely site of CSF leak is on the left, with fluid tracking along the left S1, and to a lesser degree L5, nerve roots.

Case Discussion

This patient has a known and confirmed history of Marfan's disease. CSF leak from meningocoeles is recognised as a cause of spontaneous intracranial hypotension

Unfortunately follow-up is not available. 

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Case Information

rID: 43216
Case created: 29th Feb 2016
Last edited: 21st Apr 2017
Inclusion in quiz mode: Included

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