Cystic fibrosis

Case contributed by Dr Mohammad Ashkan Moslehi

Presentation

10 y/o boy a case of CF with end stage lung involvement

Patient Data

Age: 10
Gender: Male
X-ray

The lungs are hyperaerated.

Bilateral reticulonodular infiltration is seen, along with cystic lesions, suggesting bronchiectasis (more prominent in upper zones). Consolidation is seen in left lower lobe.

Case Discussion

The patient died due to severe respiratory failure

Chest x-rays are insensitive to the early changes of cystic fibrosis, with changes seen on HRCT in 65% of patients with CF and normal CXR1.  Later changes on x-rays include:

  • bronchiectasis;
  • hyperinflation;
  • lobar collapse;
  • pulmonary arterial enlargement due to pulmonary arterial hypertension is seen in patients with long standing disease;
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Case information

rID: 19086
Case created: 5th Aug 2012
Last edited: 24th Dec 2016
Systems: Chest, Paediatrics
Inclusion in quiz mode: Included

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