Presentation
10 years old boy with a known chronic condition.
Patient Data
Age: 10
Gender: Male
From the case:
Cystic fibrosis
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The lungs are hyperaerated.
Bilateral reticulonodular infiltration is seen, along with cystic lesions, suggesting bronchiectasis (more prominent in upper zones). Consolidation is seen in left lower lobe.
Case Discussion
The patient died due to severe respiratory failure.
Chest x-rays are insensitive to the early changes of cystic fibrosis, with changes seen on HRCT in 65% of patients with CF and normal CXR1. Later changes on x-rays include:
- bronchiectasis;
- hyperinflation;
- lobar collapse;
- pulmonary arterial enlargement due to pulmonary arterial hypertension is seen in patients with long standing disease;