Cystic fibrosis

Case contributed by Dr Amro Omar

Presentation

Chronic pulmonary symptoms , meconium ileus at birth

Patient Data

Gender: Male
Modality: X-ray

Imaged in 2011

Diffuse reticulonodular changes with bronchiectasis and prominent hila. Lung volume is preserved.

Modality: CT

2013 study:

Scout image shows finger in glove appearance .

On CT, note the tree in bud pattern nodules, the cylinderical bronchiectasis, and the mucous plugs.

Associated abnormalities in cystic fibrosis:

  • exocrine pancreatic insufficiency
  • pansinusitis
    • almost all will have underdeveloped & opacified paranasal sinuses on imaging
  • biliary cirrhosis
  • bone demineralization
    • compression fractures are common
    • rib fractures
  • infertility
  • high association with meconium ileus at birth

Case Discussion

Consider cystic fibrosis in any young adult with unexplained bronchiectasis.

For a young adult with diffuse bronchiectasis and interstitial lung disease, consider cystic fibrosis until proven otherwise.

 

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Case Information

rID: 32436
Case created: 26th Nov 2014
Last edited: 1st Oct 2015
Systems: Chest, Paediatrics
Inclusion in quiz mode: Included

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