Cystic fibrosis

Case contributed by Dr Abdallah Khateeb

Presentation

Known case of a congenital disorder. Developed respiratory decompensation.

Patient Data

Age: 22-year-old
Gender: Male
X-ray

Findings of advanced bilateral bronchiectasis; ring shadows, tram-track lines and ill defined vascular markings.

CT

Better definition of the changes are seen on the CT scan. Cylinderical, varicose and cystic bronchiectasis are well demonstrated. Peribronchial thickening and multiple ground glass opacities.

Case Discussion

This patient has cystic fibrosis. Other findings seen on this case related to cystic fibrosis include:

  • extensive pancreatic parenchymal fatty replacement
  • numerous hypodense nodules involving the liver, separated by bands of residual parenchyma, which is best explained by cirrhosis with multiple regenerative nodules
  • splenomegaly with multiple prominent venous channels at its hilum, with a prominent portal system; changes of portal hypertension.
  • thin patient
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Case information

rID: 44945
Case created: 9th May 2016
Last edited: 9th May 2017
System: Chest
Inclusion in quiz mode: Included

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