Presentation
Known case of cystic fibrosis, complicated with ABPA and chronic Staphylococcus aureus infection.
Patient Data
Age: 10 years
Gender: Female
From the case:
Cystic fibrosis
Download
Info
The tip of the port catheter is seen at the confluence of the SVC and brachiocephalic veins.
Extensive bilateral fusiform and cystic bronchiectasis, bronchial wall thickening, and endobronchial mucous plugging, more marked in the right lung. Both lungs are hyperinflated. Peribronchial patchy consolidation.
Case Discussion
Pulmonary manifestations of cystic fibrosis classically include chronic bronchiectasis with bronchial wall thickening and endobronchial mucus plugging.
This girl presented with an acute exacerbation of chest infection and was due to commence cystic fibrosis transmembrane conductance regulator (CFTR) treatment.
Unable to process the form. Check for errors and try again.