Dandy Walker malformation

Case contributed by Dr Sepehr Haghighi

Presentation

A boy with ataxia and developmental delay

Patient Data

Age: 20 months
Gender: Male
MRI

Evidence of vermis aplasia associated with enlarged posterior fossa and  torcular-lambdoid inversion is seen. Cystic dilation of 4th ventricle is also noted. 

These findings are compatible with Dandy Walker Malformation.

Case Discussion

This is a classic case of a Dandy Walker malformation.

  • hypoplasia of the vermis and cephalad rotation of the vermian remnant
  • cystic dilatation of the fourth ventricle extending posteriorly 
  • enlarged posterior fossa with torcular-lambdoid inversion (torcular lying above the level of the lambdoid due to abnormally high tentorium
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Case information

rID: 65606
Published: 22nd Jan 2019
Last edited: 24th Jan 2019
Inclusion in quiz mode: Included
Excluded from licensing
Institution: Children's medical center

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