Dandy-Walker malformation

Case contributed by Ammar Haouimi
Diagnosis certain

Presentation

Large head circumference.

Patient Data

Age: 6 months
Gender: Female
ct

The posterior fossa is enlarged with a  trocular lying above the level of the lambdoid  (torcular-lambdoid inversion). There is a cystic dilatation of the 4th ventricle extending posteriorly forming a cystic space with an anterolateral displacement of the cerebellar hemispheres. Hypoplasia of the vermis with a cephalad rotation of the small vermian remnant. Gross hydrocephalus secondary to the posterior fossa abnormalities, 

 

Case Discussion

CT features are consistent with a Dandy-Walker malformation.

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