Dandy Walker malformation

Patient Data

Age: 13 years
Gender: Female

Large cystic area in the posterior fossa extending upto the fourth ventricle. Partial agenesis of the cerebellar vermis, which is superiorly placed. Cystic dilatation of the third and lateral ventricles. Hypodensity noted in periventricular white matter. Posterior fontanelle is still not fused.

Case Discussion

Dandy Walker malformation consists of a group of anomalies where there is a posterior fossa cyst communicates with the fourth ventricle, as well as abnormal development of the cerebellar vermis.

In its classical presentation consists of the triad of:

  1. Hypoplasia of the vermis and cephalad rotation of the vermian remnant
  2. Cystic dilatation of the fourth ventricle extending posteriorly. Usually the cerebellar hemispheres are displaced anterolaterally, but with a normal size and morphology
  3. Enlarged posterior fossa with torcular-lambdoid inversion
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Case information

rID: 38180
Case created: 9th Jul 2015
Last edited: 16th Dec 2015
Inclusion in quiz mode: Included

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