Dandy-Walker variant

Case contributed by Dr Mohammad A. ElBeialy

Presentation

Large head size with convulsions. Prenatal U/S shows hydrocephalus.

Patient Data

Age: 1 month
Gender: Female
Modality: CT
  • moderate supratentorial dilatation of the ventricular system. The bodies of the lateral ventricles are widely separated and parallel with high-riding 3rd ventricle. 
  • mega cisterna magna with retro-cerebellar cystic lesion of CSF density communicating with the 4th ventricle.
  • hypoplasia of the cerebellar vermis. 
  • no mass lesion or parenchymal area of abnormal attenuation. 
  • normal cortical sulci. 
  • no extra-axial collection. 
Diagnosis:
Dandy-Walker variant with moderate supratentorial hydrocephalus and mega cisterna magna as well as retro-cerebellar cyst communicating with the 4th ventricle through hypoplastic vermis. Associated agenesis of the corpus callosum.

Case Discussion

Dandy-Walker variant is associated with variable degrees of vermian hypoplasia. A retrocerebellar cyst is seen communicating with the 4th ventricle with supratentorial hydrocephalus. Association with agenesis of the corpus callosum is common. DW variant is more common than DW malformation.
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Case Information

rID: 23039
Case created: 16th May 2013
Last edited: 24th Feb 2016
Inclusion in quiz mode: Included

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